Paediatric Restrictive Cardiomyopathy - Diagnosis and Challenges
نویسندگان
چکیده
Restrictive cardiomyopathy is one of the rarest forms cardiomyopathies in pediatric patients characterized by impaired myocardial relaxation or compliance with restricted ventricular filling, leading to a reduced diastolic volume preserved systolic function. We report two cases – 5-year-old boy who presented abdominal distension and palpitation family history similar complaints but no definite genetic diagnosis as yet, girl chronic cough shortness breath. Both were diagnosed Sultan Qaboos University Hospital 2019 are managed supportively regular outpatient follow-up. This first series reported restrictive from Oman.
 Keywords: cardiomyopathy, children, heart failure children.
منابع مشابه
Restrictive Cardiomyopathy
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ژورنال
عنوان ژورنال: Sultan Qaboos University Medical Journal
سال: 2023
ISSN: ['2075-0528', '2075-051X']
DOI: https://doi.org/10.18295/squmj.9.2023.055